Ecchordosis physaliphora (Concept Id: C0266493) - National Center for Ecchordosis physaliphora- Rare Retroclival Pathology Ecchordosis physaliphora | Changeset | Radiopaedia.org Ecchordosis physaliphora and its variants: proposed new - DeepDyve However, few symptomatic cases have been reported. Third type of EP variant only harbours lesions within the clivus. We describe these 2 entities and their differential diagnoses, clinical courses, and management. it passes through the basal mesoderm just cephalad to the tip of the notochord to meet the precursor of the posterior pituitary, which forms from a diverticulum of the diencephalon. Differential diagnosis: Chordoma, chondrosarcoma, metastasis, Ecchordosis Physaliphora . Ecchordosis physaliphora is a congenital, benign lesion originating from notochordal remnants along the craniospinal axis, most frequently located at the level of the clivus and sacrum.1,2 Ecchordosis physaliphora is a rare lesion and can be difficult to recog-nise and treat.1,3-5 We present three cases of previously undiagnosed ecchordosis Methods Ecchordosis physaliphora (EP) is a distinct clinical entity defined as a notochordal remnant found on the dorsal surface of the clivus, occurring in about 2 % of autopsies. Ecchordosis physaliphora is usually asymptomatic. Overview Fingerprint Abstract OBJECTIVE: Purely intradural clival chordomas are rare neoplasms, and only a few cases have been reported. Ecchordosis physaliphora is a congenital benign hamartoma tous lesion derived from notochord remnants, usually located in the retroclival prepontine region, but can be found anywhere from the skull base to the sacrum. The lesion demonstrates diffusion restriction, some degree of hemorrhagic change, and a component of T1 precontrast hyperintensity. EP is usually discovered incidentally, during autopsies or radiological studies, as a serendipity [6, 8, 23, 26, 37].It can be found anywhere along the midline craniospinal axis, from the dorsum sellae to the coccyx []; however, the most common location is the dorsal midline . Under the electron microscope, the intracellular vacuoles have a smooth limiting membrane whereas the extracellular . Ecchordosis physaliphora is usually asymptomatic. [6, 7] rarely it can be located in the sacrococcygeal region. Ecchordosis Physaliphora was first described by Hubert von Luschka in 1856 as a pathologic ectopic notochordal tissue at the posterior clivus. It is well-known that ADC values can reflect the degree of water diffusion inside the tissue, and low ADC values are indicative of restricted diffusion resulting from a high cellularity [29].. Our results suggest that the magnetic resonance imaging appearance of EP is diverse. (NCI Thesaurus) YOU MAY ALSO LIKE Eccentrocyte Count Ecchordosis physaliphora (EP) is a rare, benign, hamartomatous notochordal remnant, which is found incidentally in only 0.5%-2% of autopsies1, 2, 3 and 1.7% of thin-section, transverse, T2-weighted images of the skull base. They are found in ~2% of autopsies 1. Ecchordosis physaliphora is a small, gelatinous tissue that is considered an ectopic notochordal remnant. AJNR Am J Neuroradiol 2004; 25: 1851-1855. Described as tiny,. They are found in ~2% of autopsies 1. Morphologically it is characterized by the presence of typical physaliphorous cells in a myxoid background. Typically well-marginated without aggressive features . Discussion: More discussion of chordomas can be found here and here. May have an osseous stalk connecting the clival and intradural components . 9 Mehnert F, Beschorner R, Kuker W, Hahn U, Nagele T. Retroclival ecchordosis physaliphora: MR imaging and review of the literature. Farlex Partner Medical Dictionary Farlex 2012 Ecchordosis physaliphora (EP) is a small, gelatinous tissue that is considered an ectopic notochordal remnant ( 1 - 4 ). After the embryogenesis Ecchordosis . Ecchordosis physaliphora is a rare congenital benign hamartomatous lesion originating from nodal cord remnants. Unfortunately, ecchordosis physaliphora and chordoma are histologically indistinguishable, other than by examining the margins, the latter demonstrating infiltrative growth. At surgery, a cystic gelatinous nodule was found ventral to the pons, contiguous with the dorsal wall of the clivus via a . Monday, August 24, 2009 Neuroradiology , Teleradiology Ecchordosis physaliphora is a rare congenital, benign, hamartomatous, retroclival mass derived from notochordal tissue that is typically located intradurally in the prepontine cistern. This is histopathologically indistinguishable from chordoma, and hence imaging plays a key role in diagnosis. classical EP, incomplete EP (EP bud) and EP variant. Ecchordosis physaliphora (EP) is a benign notochordal remnant that is usually asymptomatic; symptomatic cases are extremely rare. On the post-contrast T1 scan, there was no enhancement within the lesion (Figure 4). Pathology Ecchordosis physaliphora arise from remaining notochord cells along the axis of the spine after embryogenesis. The tumor, ecchordosis physaliphora (EP), is an uncommon congenital benign hamartomatous-type which is detected for about 2% of post-mortem examinations [4, 5]. We report a case of ecchordosis physaliphora, an uncommon benign lesion originating from embryonic notochordal remnants, intradurally located in the prepontine cistern, that unusually presented associated with symptoms. Ecchordosis Physaliphora (EP), which is an uncommon . Medline, Google Scholar; 10 Akimoto J, Takeda H, Hashimoto T, Haraoka J, Ito H. A surgical case of ecchordosis physaliphora [in Japanese]. 2009 Morphologically, ecchordosis closely resembles notochord and chordoma. These lesions are hypointense on T1-weighted and hyperintense on T2-weighted images, and follow CSF signal. [2, 8] the intracranial location is within the subdural and subarachnoid space in the prepontine cistern Ecchordosis physaliphora (69664005); Heterotopic notochordal tissue (69664005) Definition. Ecchordosis physaliphora (EP) is a distinct clinical entity defined as a notochordal remnant found on the dorsal surface of the clivus, occurring in about 2 % of autopsies. Ecchordosis physaliphora (EP) is an extremely rare hamartomatous lesion characteristically located in the . Morphologically it is characterized National Institutes of Health Create Alert Papers overview Semantic Scholar uses AI to extract papers important to this topic. Cystic mass, most commonly located along the dorsal aspect of the clivus. Ecchordosis physaliphora (EP) is a retroclival notochordal remnant seen in 2% of the autopsy cases. Contrast enhanced T1 weighted MR images were obtained and showed no enhancement (Fig 2A). We report complete resection of an asymptomatic, extradural EP in the sphenoid sinus using an endoscopic transsphenoidal approach and review surgical approaches to resection. Ecchordosis physaliphora (EP) is a benign, uncommon, congenital lesion arising from vestigial notochordal remnants. The patient complained of a headache with no other neurological abnormalities. Pathology Ecchordosis physaliphora arise from remaining notochord cells along the axis of the spine after embryogenesis. Key Points Ecchordosis physaliphora (EP) is a rare benign cystic congenital lesion arising from notochord. Ecchordosis Physaliphora A very rare, slow growing, usually asymptomatic hamartomatous lesion that arises from ectopic notochordal tissue.